D81.81

Biotin-dependent carboxylase deficiency

Diagnosis reference

Nonbillable category

This entry is a category or subcategory. Choose the appropriate billable descendant based on the clinical documentation.

Effective periodOctober 1, 2026–September 30, 2027

SourceCMS ICD-10-CM order file

ClassificationDiagnosis · clinical modification

Related entries

Up to 30 descendants in this category

CODE	DESCRIPTION	TYPE
D81.810	Biotinidase deficiency	Billable
D81.818	Other biotin-dependent carboxylase deficiency	Billable
D81.819	Biotin-dependent carboxylase deficiency, unspecified	Billable

Use the complete reference

This reference does not reproduce the full tabular hierarchy, inclusion notes, Excludes1/2 notes, sequencing instructions, or seventh-character rules. Review the official tables and coding guidelines.

Open official CMS files

ICD-10-CM codes describe diagnoses. They do not have an independent Medicare PFS reimbursement amount, and billability alone does not establish coverage.