ICD-10-CM · FY 2026 APRIL UPDATE
E71.1
Other disorders of branched-chain amino-acid metabolism
Diagnosis reference
Nonbillable categoryThis entry is a category or subcategory. Choose the appropriate billable descendant based on the clinical documentation.
Effective periodOctober 1, 2026–September 30, 2027
SourceCMS ICD-10-CM order file
ClassificationDiagnosis · clinical modification
Related entries
Up to 30 descendants in this category
| CODE | DESCRIPTION | TYPE |
|---|---|---|
| E71.11 | Branched-chain organic acidurias | Category |
| E71.110 | Isovaleric acidemia | Billable |
| E71.111 | 3-methylglutaconic aciduria | Billable |
| E71.118 | Other branched-chain organic acidurias | Billable |
| E71.12 | Disorders of propionate metabolism | Category |
| E71.120 | Methylmalonic acidemia | Billable |
| E71.121 | Propionic acidemia | Billable |
| E71.128 | Other disorders of propionate metabolism | Billable |
| E71.19 | Other disorders of branched-chain amino-acid metabolism | Billable |
Use the complete reference
This reference does not reproduce the full tabular hierarchy, inclusion notes, Excludes1/2 notes, sequencing instructions, or seventh-character rules. Review the official tables and coding guidelines.
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