ICD-10-CM · FY 2026 APRIL UPDATE
E75.2
Other sphingolipidosis
Diagnosis reference
Nonbillable categoryThis entry is a category or subcategory. Choose the appropriate billable descendant based on the clinical documentation.
Effective periodOctober 1, 2026–September 30, 2027
SourceCMS ICD-10-CM order file
ClassificationDiagnosis · clinical modification
Related entries
Up to 30 descendants in this category
| CODE | DESCRIPTION | TYPE |
|---|---|---|
| E75.21 | Fabry (-Anderson) disease | Billable |
| E75.22 | Gaucher disease | Billable |
| E75.23 | Krabbe disease | Billable |
| E75.24 | Niemann-Pick disease | Category |
| E75.240 | Niemann-Pick disease type A | Billable |
| E75.241 | Niemann-Pick disease type B | Billable |
| E75.242 | Niemann-Pick disease type C | Billable |
| E75.243 | Niemann-Pick disease type D | Billable |
| E75.244 | Niemann-Pick disease type A/B | Billable |
| E75.248 | Other Niemann-Pick disease | Billable |
| E75.249 | Niemann-Pick disease, unspecified | Billable |
| E75.25 | Metachromatic leukodystrophy | Billable |
| E75.26 | Sulfatase deficiency | Billable |
| E75.27 | Pelizaeus-Merzbacher disease | Billable |
| E75.28 | Canavan disease | Billable |
| E75.29 | Other sphingolipidosis | Billable |
Use the complete reference
This reference does not reproduce the full tabular hierarchy, inclusion notes, Excludes1/2 notes, sequencing instructions, or seventh-character rules. Review the official tables and coding guidelines.
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