ICD-10-CM · FY 2026 APRIL UPDATE
E76
Disorders of glycosaminoglycan metabolism
Diagnosis reference
Nonbillable categoryThis entry is a category or subcategory. Choose the appropriate billable descendant based on the clinical documentation.
Effective periodOctober 1, 2026–September 30, 2027
SourceCMS ICD-10-CM order file
ClassificationDiagnosis · clinical modification
Related entries
Up to 30 descendants in this category
| CODE | DESCRIPTION | TYPE |
|---|---|---|
| E76.0 | Mucopolysaccharidosis, type I | Category |
| E76.01 | Hurler's syndrome | Billable |
| E76.02 | Hurler-Scheie syndrome | Billable |
| E76.03 | Scheie's syndrome | Billable |
| E76.1 | Mucopolysaccharidosis, type II | Billable |
| E76.2 | Other mucopolysaccharidoses | Category |
| E76.21 | Morquio mucopolysaccharidoses | Category |
| E76.210 | Morquio A mucopolysaccharidoses | Billable |
| E76.211 | Morquio B mucopolysaccharidoses | Billable |
| E76.219 | Morquio mucopolysaccharidoses, unspecified | Billable |
| E76.22 | Sanfilippo mucopolysaccharidoses | Billable |
| E76.29 | Other mucopolysaccharidoses | Billable |
| E76.3 | Mucopolysaccharidosis, unspecified | Billable |
| E76.8 | Other disorders of glucosaminoglycan metabolism | Billable |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | Billable |
Use the complete reference
This reference does not reproduce the full tabular hierarchy, inclusion notes, Excludes1/2 notes, sequencing instructions, or seventh-character rules. Review the official tables and coding guidelines.
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